To explore the clinical features, treatment and prognosis of neonatal congenital intestinal malrotation.

From December 2008 to December 2017, 65 patients were treated for malrotation of intestine in People′s Hospital of Xinjiang Uygur Autonomous Region pediatric surgery.65 cases, of children surgical age is 2days to 28 days(the mean operative age was 7±1.2 days). All children were confirmed as congenital intestinal malrotation by intraoperative or preoperative auxiliary examination.Sixty patients developed intermittent vomiting with gastroesophageal reflux after birth.55 patients were intermittent biliary vomiting.Five patients showed hematochezia.All children underwent color Doppler examination before surgery.There were 45 cases of positive.60 patients completed digestive angiography before surgery.There were 92% of positive.Sixty-five patients underwent Ladd′s surgery.

Sixty-five patients confirmed congenital intestinal malrotation during surgery.There are 5 patients with midgut torsion.2 cases had intestinal torsion and intestinal necrosis, accepted intestinal resection of intestinal anastomosis.One patient had congenital chylomicrons.Twenty patients combined with other gastrointestinal malformations.Intestinal torsion in children with clinical features are bloody stools, meningitis signs.

Intermittent vomiting with gastroesophageal reflux is the main manifestation of congenital intestinal malrotation.Bloody stool with peritonitis signs is a clear indication of emergency surgery.Gastrointestinal imaging is more accurate than color Doppler.Neonatal congenital intestinal malrotation complete Ladd surgery in time.Surgical effect is good, the prognosis is good.